fa عمومى General گزارش مورد case report The agenesis of corpus callosum (ACC) is referred to a complete or partial defect in the formation of corpus callosum which is a commissure between brain hemispheres. It is a rare disease that can produce a wide range of syndromes and symptoms. We present a case of newborn baby Iranian girl who had agenesis of corpus callosum. Severe atrophy of brain and Intraventricular hemorrhage in the preterm neonate was reported. Dilation of lateral ventricles and third ventricle, as well as moderate hydrocephaly and subdural effusion, were recorded in medical ultrasound studies. The brain CT scan also indicated Intraventricular hemorrhage (grade IV) and severe brain atrophy. Agenesis Of Corpus Callosum, Intraventricular Hemorrhage, Brain Atrophy, Birth Defect. 72 77 http://intjmi.com/browse.php?a_code=A-10-1-277&slc_lang=fa&sid=1 Vahid Mogharab 10031947532846003190 10031947532846003190 No Pediatrician. Department of Pediatrics, Jahrom University of Medical Sciences, Jahrom, Iran. Farshid Javdani 10031947532846003191 10031947532846003191 No Student Research Committee, Jahrom University of Medical Sciences, Jahrom, Iran. Naser Hatami 10031947532846003192 10031947532846003192 Yes Student Research Committee, Jahrom University of Medical Sciences, Jahrom, Iran. Pouyan Keshavarz 10031947532846003193 10031947532846003193 No Student Research Committee, Jahrom University of Medical Sciences, Jahrom, Iran.